This one-of-a-kind guide offers easy-to-understand explanations, advice, and management options for patients or parents of patients with cystic fibrosis. The book explains the disease process, outlines the fundamentals of diagnosing and screening, and addresses the challenges of treatment for those living with CF. As one reviewer said, this book ;is the only complete answer book for everyone living with the disease. It is an indispensable resource for families of children with CF, adolescent and adult patients, and physicians, nurses, respiratory therapists, and social workers involved in the care of CF patients. ;

 Contributing Authors v Preface vii Acknowledgments ix Introduction xiii 1 The Basic Defect 1 Daniel J. Weiner, Raymond A. Frizzell, and David M. Orenstein 2 Making the Diagnosis 13 Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner 3 The Respiratory System 21 Daniel J. Weiner and David M. Orenstein 4 The Gastrointestinal Tract 83 Douglas S. Lindblad, Daniel J. Weiner, and David M. Orenstein 5 Other Systems 103 Daniel J. Weiner and David M. Orenstein 6 Nutrition 113 Judith A. Fulton, Iris Yann, Daniel J. Weiner, and David M. Orenstein 7 Hospitalization and Other Special Treatments 135 Jonathan E. Spahr, David M. Orenstein, Daniel J. Weiner, and Louise T. Bauer 8 Transplantation 153 Geoffrey Kurland, Jonathan E. Spahr, Daniel J. Weiner, and David M. Orenstein 9 Daily Life 195 Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner 10 Exercise 205 David M. Orenstein and Daniel J. Weiner 11 Genetics 221 Barbara Karczeski, Garry R. Cutting, and David M. Orenstein 12 The Family 235 David M. Orenstein and Daniel J. Weiner 13 The Teenage Years 245 Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner 14 Cystic Fibrosis and Adulthood 265 Joseph M. Piliewski, David M. Orenstein, Jonathan E. Spahr, and Daniel J. Weiner 15 Death and Cystic Fibrosis 287 Elisabeth P. Dellon and David M. Orenstein 16 Research and Future Treatments 295 Christopher Penland, David M. Orenstein, and Daniel J. Weiner 17 The Cystic Fibrosis Foundation 311 Robert J. Beall A P P E N D I C E S A Glossary of Terms 319 B Medications 325 C Airway Clearance Techniques 363 D Some High Calorie Recipes 375 E The History of Cystic Fibrosis 385 F Bibliography and Resources 387 G Cystic Fibrosis Care Centers in the United States 391 H Cystic Fibrosis Care Centers Worldwide 411 Index 445